DISK EDEMA IN ASSOCIATION WITH HUNTERS SYNDROME - OCULAR HISTOPATHOLOGICAL FINDINGS
DISK EDEMA IN ASSOCIATION WITH HUNTERS SYNDROME - OCULAR HISTOPATHOLOGICAL FINDINGS
复制标题
DOI：
10.1136/bjo.68.8.590
复制
发表时间：
1984-01-01
影响因子：
4.1
通讯作者：
COLE, G
中科院分区：
文献类型：
--
作者：
BECK, M;COLE, G
本文报告了一名亨特氏综合征患者的后半眼和视神经的组织病理学，该患者在11年的生命中一直患有椎间盘水肿而没有颅内压升高。椎间盘水肿的可能发病机制进行了讨论，一个重要的促成因素是异常的粘多糖在巩膜内的沉积。这导致巩膜增厚，压迫巩膜内水平的视神经。
The histopathology of the posterior half of one eye and the optic nerves of a man with Hunter's syndrome, who was known to have disc oedema without raised intracranial pressure for 11 years of his life, is reported. The possible pathogenesis of the disc oedema is discussed; an important contributory factor was the deposition of abnormal mucopolysaccharides within the sclera. This caused gross thickening of the sclera with compression of the optic nerve at the intrascleral level.