CONGENITAL STATIONARY NIGHT BLINDNESS WITH NEGATIVE ELECTRORETINOGRAM - A NEW CLASSIFICATION
CONGENITAL STATIONARY NIGHT BLINDNESS WITH NEGATIVE ELECTRORETINOGRAM - A NEW CLASSIFICATION
复制标题
DOI：
10.1001/archopht.1986.01050190071042
复制
发表时间：
1986-07-01
影响因子：
--
通讯作者：
KANDA, T
中科院分区：
文献类型：
--
作者：
MIYAKE, Y;YAGASAKI, K;KANDA, T
对64例先天性静止性夜盲患者进行了分析，结果表明，所有患者的眼底基本正常。视网膜电图（ERG）显示正常的a波与极度减少的B波（负型）时，记录与单一的明亮白色刺激在黑暗中。我们将这些患者分为两组的基础上评价杆ERG和/或心理物理暗适应测量11.degree。测试目标在15 °。在视网膜的上部。一组（35例患者）缺乏棒功能（完全型），另一组（20例患者）显示出一定的棒功能（不完全型）。9名患者无法分类。没有一个家系显示一个完整型和一个不完整型。两组在屈光不正、明视功能和ERG振荡电位方面的差异提示不同的发病机制。我们的分析可能提供一个新的分类先天性静止性夜盲与负ERG。
An analysis of 64 patients with congenital stationary night blindness showed that all had essentially normal fundi. Electroretinography (ERG) showed a normal a wave with extremely reduced b wave (negative type) when recorded with a single bright white stimulus in the dark. We classified these patients into two groups based on the evaluation of rod ERG and/or psychophysical dark adaptation measured with an 11.degree. test target at 15.degree. in the upper part of the retina. One group (35 patients) lacked rod function (complete type) and the other group (20 patients) showed some rod function (incomplete type). Nine patients could not be classified. No pedigree showed a complete and incomplete type in one family. Differences between the two groups in refractive error, photopic function, and oscillatory potentials in the ERG suggest a different pathogenesis. Our analysis may provide a new classification of congenital stationary night blindness with a negative ERG.