Difficulty in Selecting the Motor Source in Dynamic Reconstruction with Latissimus Dorsi Myocutaneous Free Flap for Facial Nerve Palsy due to Möbius Syndrome
Difficulty in Selecting the Motor Source in Dynamic Reconstruction with Latissimus Dorsi Myocutaneous Free Flap for Facial Nerve Palsy due to Möbius Syndrome
复制标题
面神经麻痹背阔肌游离皮瓣动态重建运动源选择困难
DOI：
10.11270/jjsrm.28.134
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发表时间：
2015
期刊：
影响因子：
--
通讯作者：
倉林孝之
中科院分区：
文献类型：
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作者：
菅剛史;朝戸裕貴;鈴木康俊;梅川浩平;倉林孝之
莫比乌斯综合征是一种先天性神经疾病，定义为双侧面神经麻痹和外展神经麻痹的组合，先天性和非进行性。病因尚不清楚，据认为，第7和第8脑神经功能障碍是由脑干发生异常、胎儿脑干缺血或基因缺失引起的。面神经麻痹的程度从瘫痪到瘫痪各不相同，运动源的选择是神经血管移植肌皮瓣动态重建的最大困难。我们经历了一个病例，我们选择舌下神经作为运动来源，用肌皮瓣进行动态重建，治疗由于Möbius综合征引起的面神经麻痹。经过7年的随访，观察到面部的对称性和自然的微笑。
Möbius syndrome, a congenital neurological disorder, is defined as the combination of bilateral facial nerve palsy and abducens nerve palsy that is congenital and nonprogressive. The etiology is unknown and it is thought that disturbances in the 7th and 8th cranial nerves are caused by abnormalities in brainstem genesis, brainstem ischemia in fetal life, or gene depletion. The degree of facial nerve palsy varies from plegia to paresis and the selection of motor source is the most difficult factor in dynamic reconstruction with neurovascular transfer of a myocutaneous free flap. We experienced a case in which we chose the hypoglossal nerve as the motor source in dynamic reconstruction with a myocutaneous free flap for facial nerve palsy due to Möbius syndrome. At 7 years of follow-up, symmetrical appearance of the face at rest with natural smiling was observed.