Prominent tongue and jaw tremor in a patient with probable Progressive Supranuclear Palsy.
Prominent tongue and jaw tremor in a patient with probable Progressive Supranuclear Palsy.
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可能患有进行性核上性麻痹的患者出现明显的舌头和下颌震颤。
DOI：
10.1002/mdc3.12562
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发表时间：
2018
影响因子：
4
通讯作者：
Litvan,Irene
中科院分区：
文献类型：
--
作者：
Shoeibi,Ali;Litvan,Irene
讨论这是首例PSP患者出现明显的舌部和颌部震颤而无腭部和四肢震颤的报告。然而，在患有PSP的患者中出现腭部震颤的报道很少。3我们的病人同时符合威廉的定义4和最近描述的可能的运动障碍协会的PSP-帕金森症标准。5表现为PD表型(轴向占优势的运动迟缓和僵直，以及L-多巴抵抗；A2)，后来转变为PSP-Richardson表型(垂直方向的自主注视范围明显受限于水平方向；O1)。
DiscussionThis is the first report of a prominent tongue and jaw tremor without palatal and limb tremor in a patient with PSP. However, there are rare reports of palatal tremor in patients who have PSP. 3 Our patient meets both the William's definition 4 and the recently described probable Movement Disorder Society PSP‐parkinsonism criteria. 5 She presented with a PD phenotype (bradykinesia and rigidity with axial predominance, and l‐dopa resistance; A2) that later converted into a PSP‐Richardson phenotype (clear limitation of the range of voluntary gaze in the vertical more than in the horizontal plane; O1).