Well-differentiated, pedunculated liposarcoma of the hypopharynx
Well-differentiated, pedunculated liposarcoma of the hypopharynx
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DOI：
10.1016/j.anorl.2017.07.001
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发表时间：
2018-02-01
影响因子：
2.5
通讯作者：
Debry, C.
中科院分区：
文献类型：
--
作者：
Eyermann, C.;Raguin, T.;Debry, C.
摘要：下咽部的脂肪肉瘤极为罕见，文献中仅报告28例。脂肪肉瘤的主要症状是逐渐恶化的吞咽困难。病例报告：作者报告的情况下，一个71岁的男子谁提出了吞咽困难，显着的体重下降超过几个星期，并发作的一个固体块从嘴里exteriorization在呕吐发作。影像学检查显示脂肪密度食管内肿块。全内窥镜和上消化道内窥镜检查显示了左侧梨状窦内的带蒂肿瘤，该肿瘤可以通过口腔取出。然后在下咽附着蒂处通过内窥镜切除肿瘤。手术标本的组织学检查得出结论分化良好的良性liposarcoma.Discussion：分化良好的脂肪肉瘤是脂肪肉瘤的最常见的形式，但只有例外的下咽部报告。主要症状与邻近结构的压迫有关。影像学表现无特异性。只有组织学检查才能区分脂肪肉瘤和其他良性食管肿瘤。标准治疗包括广泛的、完全的切除，这在颈部并不总是可能的。对这些患者进行长期随访是必要的，以便快速发现复发。(C)2017年Elsevier Masson SAS。All rights reserved.
Introduction: Liposarcoma of the hypopharynx is extremely rare, as only 28 cases have been reported in the literature. The cardinal symptom of liposarcoma is progressively worsening dysphagia.Case report: The authors report the case of a 71-year-old man who presented with dysphagia, marked weight loss over several weeks and an episode of exteriorization of a solid mass from the mouth during an episode of vomiting. Imaging revealed a fat density intra-oesophageal mass. Panendoscopy and upper gastrointestinal endoscopy visualized the pedunculated tumour in the left piriform sinus, which was able to be exteriorized via the mouth. The tumour was then resected endoscopically at its hypopharyngeal insertion pedicle. Histological examination of the operative specimen concluded on well-differentiated benign liposarcoma.Discussion: Well-differentiated liposarcoma is the most common form of liposarcoma, but is only exceptionally reported in the hypopharynx. The main symptoms are related to compression of adjacent structures. Imaging findings are nonspecific. Only histological examination can distinguish liposarcoma from other benign oesophageal tumours. Standard treatment consists of wide, complete resection, which is not always possible in the neck. Long-term follow-up of these patients is essential in order to rapidly detect recurrence. (C) 2017 Elsevier Masson SAS. All rights reserved.