SURGICAL-TREATMENT OF MOYAMOYA DISEASE - OPERATIVE TECHNIQUE FOR ENCEPHALO-DURO-ARTERIO-MYO-SYNANGIOSIS, ITS FOLLOW-UP, CLINICAL-RESULTS, AND ANGIOGRAMS
SURGICAL-TREATMENT OF MOYAMOYA DISEASE - OPERATIVE TECHNIQUE FOR ENCEPHALO-DURO-ARTERIO-MYO-SYNANGIOSIS, ITS FOLLOW-UP, CLINICAL-RESULTS, AND ANGIOGRAMS
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DOI：
10.1227/00006123-199304000-00006
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发表时间：
1993-04-01
期刊：
影响因子：
4.8
通讯作者：
KOBAYASHI, S
中科院分区：
文献类型：
--
作者：
KINUGASA, K;MANDAI, S;KOBAYASHI, S
MOYAMOYA综合征被定义为脑底部侧支吻合通路的发展，与颈动脉分叉慢性进行性狭窄相关。血管重建手术和保守策略均可用于治疗该综合征，但后者不能阻止疾病的进展。我们描述了脑硬动脉肌合症（EDAMS）的治疗过程，并报告了17例（28侧）接受EDAMS治疗的患者的结果。烟雾病的临床症状包括短暂性脑缺血发作、可逆性缺血性神经功能缺损、中风、癫痫发作、格斯特曼综合征、不自主运动或脑血流不足导致的智力迟钝。EDAMS的临床结果为1例差，2例一般，5例好，8例优，1例一边一般，另一边优异。术后血管造影显示EDAMS患者缺血脑表面有广泛的侧支循环。
MOYAMOYA SYNDROME IS defined as the development of collateral anastomosis pathways at the base of the brain, associated with chronic progressive stenosis of the carotid fork. Both reconstructive vascular surgery and conservative strategies are used to treat this syndrome, but the latter cannot prevent the disease from progressing. We describe the procedure of encephalo-duro-arterio-myo-synangiosis (EDAMS), and report the results in 17 patients (28 sides) who underwent EDAMS. The clinical symptoms of moyamoya disease include transient ischemic attacks, reversible ischemic neurological deficits, stroke, seizures, Gerstmann's syndrome, involuntary movements, or mental retardation resulting from the lack of cerebral blood flow. The clinical results of EDAMS were poor in one patient, fair in two, good in five, excellent in eight, and fair on one side and excellent on the other side in one patient. Postoperative angiograms showed widespread collateral circulation on the ischemic brain surface in patients undergoing EDAMS.