Autoimmune autonomic ganglionopathy with late-onset encephalopathy
Autoimmune autonomic ganglionopathy with late-onset encephalopathy
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DOI：
10.1016/j.autneu.2008.10.016
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发表时间：
2009-03-12
影响因子：
2.7
通讯作者：
Vernino, S.
中科院分区：
文献类型：
--
作者：
Baker, S. K.;Morillo, C.;Vernino, S.
47岁女性，有4个月的早期饱腹、便秘、光敏、直立性不耐受、瘙痒和脱水史。检查发现瞳孔扩大，无反应，眼和口干燥，但力量、相反射和感觉正常。静立3分钟后，收缩压下降70毫米汞柱，固定心率74 bpm。她的- 3神经节AChR水平为2060 pmol/L（正常）
A 47-year old female presented with a 4 month history of early satiety, constipation, light sensitivity, orthostatic intolerance, siccca, and anhydrosis. Her examination revealed dilated, unreactive pupils with dry eyes and mouth but normal strength, phasic reflexes, and sensation. After 3 min of quiet standing her systolic pressure dropped 70 mmHg with a fixed heart rate of 74 bpm. Her alpha 3 ganglionic AChR level was 2060 pmol/L (normal