Complete visual recovery in osteopetrosis by early optic nerve decompression
Complete visual recovery in osteopetrosis by early optic nerve decompression
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DOI：
10.1159/000055980
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发表时间：
2000-12-01
影响因子：
0.7
通讯作者：
Wang, KC
中科院分区：
文献类型：
--
作者：
Hwang, JM;Kim, IO;Wang, KC
视神经萎缩伴视力丧失在石骨症中很常见。视神经减压术治疗石骨症的疗效仍有争议。本研究的目的是报告早期视神经减压可以完全逆转石骨症的视力恶化。摘要一位八岁女性石骨症患者，在眼科检查中发现视力下降。行广泛视神经减压术。它不仅包括去顶视神经管，而且还钻掉视神经两侧的骨头。在同一手术过程中对两条视神经进行减压。在视力恶化的早期阶段，视神经减压可以预防与骨硬化症相关的视力逐渐丧失。在管理石骨症患者时，应强调仔细和定期评估视功能的重要性。版权所有（C）2001 S. Karger AG，巴塞尔。
Visual loss with optic atrophy is common in osteopetrosis. The efficacy of optic nerve decompression in patients with osteopetrosis is still controversial. The purpose of this study is to report that visual deterioration in osteopetrosis can be completely reversed by early optic nerve decompression. An 8-year-old female patient with osteopetrosis was found to have reduced visual acuity on routine ophthalmologic examination. Extensive optic nerve decompression was performed. It not only included unroofing the optic canal, but also drilling away bone on both sidewalls of the optic nerve. Both optic nerves were decompressed during the same surgical procedure. Progressive loss of vision associated with osteopetrosis can be prevented by optic nerve decompression in the early stage of visual deterioration. When managing patients with osteopetrosis, the importance of careful and regular assessment of visual function should be stressed. Copyright (C) 2001 S. Karger AG, Basel.