Cardiac sarcoidosis masquerading as right ventricular dysplasia

Cardiac sarcoidosis masquerading as right ventricular dysplasia
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DOI:
10.1046/j.1460-9592.2003.t01-1-00217.x
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发表时间:
2003-07-01
影响因子:
1.8
通讯作者:
Fuenzalida, CE
Fuenzalida, CE
中科院分区:
工程技术4区
文献类型:
--
作者:
Ott, P;Marcus, FI;Fuenzalida, CE

文献摘要

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心脏结节病患者的临床和形态特征可能类似于致心律失常性右室发育不良(ARVD)或心肌病(ARVC)。本文报告三例心脏结节病,临床上类似于ARVD或ARVC,直到活检或尸检时病理诊断为结节病。虽然通常很难做出诊断区分,但由于皮质类固醇治疗可能使结节病患者受益,但预计对ARVD或ARVC病例不起作用,因此诊断区分很重要。
Patients with cardiac sarcoidosis may present with clinical and morphological features similar to arrhythmogenic right ventricular dysplasia (ARVD) or cardiomyopothy (ARVC). Three cases of cardiac sarcoidosis are presented that clinically mimicked ARVD or ARVC until a pathology diagnosis of sarcoidosis was made at biopsy or autopsy. A diagnostic distinction, while often difficult to make, is important since treatment with corticosteroids may benefit those with sarcoidosis but is not expected to be useful in cases with ARVD or ARVC.