Sudden death in hypertrophic cardiomyopathy with normal left ventricular mass.
Sudden death in hypertrophic cardiomyopathy with normal left ventricular mass.
复制标题
左心室质量正常的肥厚性心肌病猝死。
作者：
Barry J. Maron;A. H. Kragel;W. C. Roberts
一名活跃、健康、无症状的16岁男孩，有肥厚型心肌病家族病史，在放学回家的路上突然死亡。尸检显示无左室肥厚(即正常心脏重量)，但肥厚型心肌病的组织学特征异常，如心肌细胞紊乱和壁内冠状动脉异常。这位患者很可能患有肥厚性心肌病，在左心室肥厚发展之前死亡。
An active, healthy, and symptom free 16 year old boy with a family history of hypertrophic cardiomyopathy died suddenly while walking home from school. Necropsy showed absence of left ventricular hypertrophy (that is, normal heart weight), though the characteristic histological abnormalities of hypertrophic cardiomyopathy, such as cardiac muscle cell disorganisation and abnormal intramural coronary arteries, were present. It is likely that this patient had hypertrophic cardiomyopathy and died before left ventricular hypertrophy developed.