Bilateral persistent hyperplastic primary vitreous.
Bilateral persistent hyperplastic primary vitreous.
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DOI：
10.1111/j.1440-1673.2005.01402.x
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发表时间：
2005-02-01
期刊：
影响因子：
--
通讯作者：
Purandare, N C
中科院分区：
文献类型：
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作者：
Sanghvi, D A;Sanghvi, C A;Purandare, N C
我们报告一例5个月大的婴儿出现双侧白斑的双侧持续性增殖性原发性玻璃体（PHPV）。该儿童因临床怀疑视网膜母细胞瘤而接受眼部超声检查。灰度评价显示左侧眼球后段有回声带，从晶状体囊后表面延伸到视盘。多普勒检查显示带内有血流。对侧球的超声检查显示在与视盘接触的后段有高回声组织团块。大多数PHPV病例是散发的和单侧的。双侧PHPV罕见。在Pollard对83例患者的研究中，只有2例患者（2.4%）患有双侧PHPV。本病例的影像学特征提示双侧PHPV的诊断。我们建议，这种实体，虽然罕见，应考虑在鉴别诊断，同时评估双侧白斑。
We report a case of bilateral persistent hyperplastic primary vitreous (PHPV) in a 5-month-old infant who presented with bilateral leukokoria. The child was referred for ocular ultrasound with a clinical suspicion of retinoblastoma. Grey-scale evaluation revealed an echogenic band in the posterior segment of the left globe extending from the posterior surface of the lens capsule to the optic disc. Doppler examination revealed the presence of blood flow in the band. Ultrasound assessment of the contralateral globe showed an elevated mass of echogenic tissue in the posterior segment, in contact with the optic disc. Most cases of PHPV are sporadic and unilateral. Bilateral PHPV is rare. In a study by Pollard of 83 cases, only two patients (2.4%) had bilateral PHPV. The imaging features in this case point toward the diagnosis of bilateral PHPV. We suggest that this entity, although rare, should be considered in the differential diagnosis while evaluating bilateral leukokoria.