Erythromelalgia with a linear pattern in a 12-year-old girl
Erythromelalgia with a linear pattern in a 12-year-old girl
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DOI：
10.1111/ped.12661
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发表时间：
2015-08-01
影响因子：
1.4
通讯作者：
Choi, Jae Young
中科院分区：
文献类型：
--
作者：
Huh, Seokwon;Jung, Mo Kyung;Choi, Jae Young
红斑性肢痛症是一种罕见的临床综合征，其特征是红斑、体温升高和严重的烧灼痛，这些疼痛可因温暖而加重或因寒冷而减轻。红斑性肢痛症是一种原发性、特发性形式，或继发于许多疾病和病症。虽然在成人中进行了相当好的研究，但儿科年龄组的特征，发病机制和自然史的特征很差。已经尝试了不同的治疗方案，但没有最佳治疗方法已建议红斑性肢痛症。我们报告一个罕见的线性红斑性肢痛症的12岁女孩，涉及她的中央机构从外周四肢，这似乎是继发于血管炎。阿司匹林和普萘洛尔维持治疗的临床进展时好时坏。
Erythromelalgia is a rare clinical syndrome characterized by erythema, increased temperature, and severe burning pain that can be aggravated by warmth or relieved by cold. Erythromelalgia occurs either as a primary, idiopathic form, or secondary to a number of diseases and conditions. Although fairly well studied in adults, the characteristics, pathogenesis, and natural history are poorly characterized in the pediatric age group. Different therapeutic options have been tried, but no optimal treatment has been suggested for erythromelalgia. We report a rare case of linear erythromelalgia in a 12-year-old girl involving her central body from the peripheral extremities, which seemed to be secondary due to vasculitis. Clinical progress waxed and waned on maintenance aspirin and propranolol.