A case report of congenital scoliosis associated with situs inversus totalis.
A case report of congenital scoliosis associated with situs inversus totalis.
复制标题
伴有全反位的先天性脊柱侧凸一例报告
DOI：
10.1097/md.0000000000009239
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发表时间：
2017-12
期刊：
影响因子：
1.6
通讯作者：
Song Y
中科院分区：
文献类型：
--
作者：
Zhu C;Huang S;Zhou C;Yang X;Wang L;Ling T;Liu L;Song Y
基本原理：全反位是一种罕见的异常疾病，其中胸部和腹部的器官位于正常位置的镜像反转。虽然这已被证实与脊柱畸形有关，但关于先天性脊柱侧凸的全反位的报道仍然有限。患者问题：我们报告一个9岁的女孩，患有先天性脊柱侧凸并伴有全反位。诊断：她也有其他相关的异常：室间隔缺损，轻度限制性排尿功能障碍，肾积水和脊髓灰质炎。术前Cobb角（T11-L3）为78°。干预措施：她接受了单根生长棒治疗，随后接受了脊柱侧凸后路脊柱融合矫正手术。成果：术后主弯冠状面Cobb角矫正至20°，矫正术后1年脊柱矫正角无明显丢失。经验教训：生长棒技术可能是治疗脊柱侧凸伴完全性体位倒置的一种安全有效的替代方法。在对这类患者进行左侧腰椎弯曲矫正时，在凹侧放置椎弓根螺钉时，不应忽视主动脉撞击的风险。
Rationale: Situs inversus totalis is a rare anomaly disease in which the organs in the chest and abdomen are positioned in a mirror image reversal of normal positions. Although this has been confirmed to be associated with spinal abnormalities, reports about situs inversus totalis with congenital scoliosis remain limited. Patient concerns: We present a 9-year-old girl having congenital scoliosis associated with situs inversus totalis. Diagnoses: She also had other associated anomalies: ventricular septal defect, mild restrictive ventilatory dysfunction, hydronephrosis, and syringomyelia. Her preoperative Cobb angle (T11–L3) was 78°. Interventions: She received single growing rods treatment and subsequent posterior spinal fusion correction surgery for her scoliosis. Outcomes: The coronal Cobb angle of the main curve was corrected to 20° postoperatively and no obvious loss of spinal corrective angle was identified 1 year after the correction surgery. Lessons: Growing rods technique could be a safe and effective alternative for the treatment of scoliosis associated with situs inversus totalis. In the correction of left-sided lumbar curve of this kind of patients, the risks of aorta impingements should not be neglected when placing pedicle screws on the concave sides.