Recommendations from the Association for European Paediatric and Congenital Cardiology for training in pulmonary hypertension
Recommendations from the Association for European Paediatric and Congenital Cardiology for training in pulmonary hypertension
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DOI：
10.1017/s104795111900235x
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发表时间：
2019-11-01
影响因子：
1
通讯作者：
Hansmann, Georg
中科院分区：
文献类型：
--
作者：
Sallmon, Hannes;Moledina, Shahin;Hansmann, Georg
肺动脉高压是一种复杂的进行性疾病，可为特发性或遗传性，或与一种或多种健康状况相关，可能伴有或不伴有先天性或获得性心血管疾病。近期的进展极大地丰富了儿童和年轻成人肺动脉高压的诊断和治疗方法，然而该疾病仍然具有较高的发病率和死亡率。这些方法包括无创成像、药物治疗、介入和手术操作以及支持性措施。针对年轻人肺动脉高压的最佳个性化诊断和治疗策略正在迅速发展，但仍然面临巨大挑战：医疗服务提供者在启动高级诊断和治疗时，需要考虑患者的年龄、发育情况、疾病状态以及家庭关注的问题。因此，需要对儿科肺动脉高压的核心和高级医学培训提供指导。欧洲儿科和先天性心脏病协会工作组“肺动脉高压、心力衰竭和移植”制定了本文件作为专家共识声明；然而，所有建议都必须结合当地和国家的基础设施以及法律法规来考虑和应用。
Pulmonary hypertension is a complex and progressive condition that is either idiopathic or heritable, or associated with one or multiple health conditions, with or without congenital or acquired cardiovascular disease. Recent developments have tremendously increased the armamentarium of diagnostic and therapeutic approaches in children and young adults with pulmonary hypertension that is still associated with a high morbidity and mortality. These modalities include non-invasive imaging, pharmacotherapy, interventional and surgical procedures, and supportive measures. The optimal, tailored diagnostic and therapeutic strategies for pulmonary hypertension in the young are rapidly evolving but still face enormous challenges: Healthcare providers need to take the patient's age, development, disease state, and family concerns into account when initiating advanced diagnostics and treatment. Therefore, there is a need for guidance on core and advanced medical training in paediatric pulmonary hypertension. The Association for European Paediatric and Congenital Cardiology working group "pulmonary hypertension, heart failure and transplantation" has produced this document as an expert consensus statement; however, all recommendations must be considered and applied in the context of the local and national infrastructure and legal regulations.