The self-concept of children and adolescents with neurofibromatosis type 1
The self-concept of children and adolescents with neurofibromatosis type 1
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DOI：
10.1111/j.1365-2214.2006.00717.x
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发表时间：
2007-07-01
影响因子：
1.9
通讯作者：
North, K.
中科院分区：
文献类型：
--
作者：
Barton, B.;North, K.
背景1型神经纤维瘤病(NF1)是一种遗传性疾病，与认知障碍、学习问题、内科并发症和美容缺陷有关。尽管NF1有广泛的影响，但很少有研究考察NF1患者的心理社会适应，特别是自我概念。本研究的目的有三个方面：(I)考察NF1儿童和青少年的自我概念；(Ii)比较NF1儿童(仅NF1)、NF1儿童和学习困难儿童[NF1+LA(低成就)]、NF1儿童和注意缺陷多动障碍儿童(NF1+ADHD)的自我概念；以及(Iii)考察这三组儿童的学业自我概念与客观标准-学业成绩和教师学业能力评分的关系。结果大多数NF1患儿的总体自我概念是积极的，但个别领域存在例外。患有NF1的儿童和青少年在身体能力方面的自我概念明显较差。与标准均值相比，青少年对数学和一般自我的自我概念也明显较差。NF1的临床严重程度不是身体外表或身体能力自我概念的显著预测因素。尽管仅NF1组、NF1+LA组和NF1+ADHD组在学业成就测量和教师学业能力评分上存在显著差异，但在学业自我概念或任何其他自我概念领域，两组之间没有显著差异。结论NF1儿童青少年在身体和运动能力方面最容易形成消极的自我概念。夸大的学术自我知觉根据积极的虚幻偏差进行了讨论，这可能是一种适应或保护功能。
Background Neurofibromatosis type 1 (NF1) is a genetic disorder associated with cognitive deficits, learning problems, medical complications and cosmetic disfigurement. Despite the wide-ranging impact of NF1, very few studies have examined the psychosocial adjustment of individuals with NF1, and in particular, self-concept. The aims of this study were threefold: (i) to examine the self-concept of children and adolescents with NF1; (ii) to compare the self-concept of children with NF1 (NF1 only), children with NF1 and learning difficulties [NF1 + LA (low achievement)], and children with NF1 and attention deficit hyperactivity disorder (ADHD) (NF1 + ADHD); and (iii) to examine the academic self-concept of these three groups relative to objective criteria - academic achievement and teacher ratings of academic competence.Methods Measures of self-concept, academic achievement and intelligence were administered to 49 children and 26 adolescents with NF1. Parents and teachers completed behavioural rating scales.Results The majority of children and adolescents with NF1 reported positive global self-concept, with some exceptions on specific domains. Children and adolescents with NF1 reported significantly poorer self-concept for physical abilities. Adolescents also reported significantly poorer self-concept for mathematics and general self when compared with normative mean values. Clinical severity of NF1 was not a significant predictor of self-concept for physical appearance or physical abilities. Despite a significant difference between NF1 only, NF1 + LA and NF1 + ADHD groups on measures of academic achievement and teacher ratings of academic competence, there was no significant difference between the groups for academic domains of self-concept, or any other domain of self-concept. All three groups reported inflated academic self-perceptions relative to objective criteria.Conclusion Children and adolescents with NF1 are most likely to develop negative self-concepts about their physical and sporting abilities. Inflated academic self-perceptions are discussed in light of the positive illusory bias, which may serve as an adaptive or protective function.