[Gelatinous dystrophy of the cornea. Apropos of 5 cases].
[Gelatinous dystrophy of the cornea. Apropos of 5 cases].
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[角膜凝胶状营养不良。
DOI：
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发表时间：
1994
期刊：
影响因子：
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通讯作者：
A. Ouertani
中科院分区：
文献类型：
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作者：
L. Lasram;C. Rais;M. El Euch;A. Ouertani
胶滴状角膜营养不良是一种罕见的疾病，由Nakaizumi（日本）于1914年首次描述。我们报告5例这种原发性角膜淀粉样变性。我们的三个病人是兄弟，另外两个病例是孤立病例。畏光和视力逐渐丧失是最先出现的症状。角膜病变通常是上皮下的双侧白色结节状沉积物。由于角膜移植物上的疾病复发，患者平均间隔5年接受重复角膜移植术。所有病例均经组织学确诊为角膜淀粉样变性。我们将我们的结果与文献报道的数据进行了比较。
Gelatinous drop-like corneal dystrophy is a rare disease, described for the first time by Nakaizumi (Japan) in 1914. We report 5 cases of this primary corneal amyloidosis. Three of our patients are brothers, the two other cases are isolated cases. Photophobia and progressive loss of vision are the first presenting signs. Corneal lesions are typically bilateral white nodular deposits beneath the epithelium. Patients underwent repeated keratoplasties with a mean interval of 5 years because of the recurrence of the disease on the corneal graft. Diagnosis of corneal amyloidosis was confirmed in all cases by histology. We compared our results with the data reported in the literature.