Two von Recklinghausen's disease cases with pheochromocytomas and gastrointestinal stromal tumors (GIST) in combination
Two von Recklinghausen's disease cases with pheochromocytomas and gastrointestinal stromal tumors (GIST) in combination
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DOI：
10.1111/j.1442-2042.2006.01601.x
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发表时间：
2007-01-01
影响因子：
2.6
通讯作者：
Narita, Makoto
中科院分区：
文献类型：
--
作者：
Teramoto, Sakiko;Ota, Tomonori;Narita, Makoto
我们在此记录两例von Reckinghausen病同时伴有嗜铬细胞瘤和胃肠道间质瘤(GIST)。这三种疾病同时发生是非常罕见的，尽管除了大肿瘤外，术前检测GIST很困难这一事实可能在这方面很重要。在目前的病例中，GIST在手术前的计算机断层扫描和磁共振成像上并不明显，在手术中意外地被发现。我们的研究结果表明，对于伴有von Reckinghausen病的嗜铬细胞瘤患者，在肾上腺切除术中应对腹膜腔进行检查。
We here document two cases of von Recklinghausen's disease with both pheochromocytomas and gastrointestinal stromal tumors (GIST). It is very rare that these three disorders are found to occur simultaneously, although the fact that preoperative detection of GIST is difficult except with large tumors may be important in this respect. In the present cases, GIST were not evident on preoperative computed tomography and magnetic resonance imaging, and were identified unexpectedly during surgery. Our findings indicate that investigation of the intraperitoneal space should be performed during adrenalectomy for pheochromocytomas with von Recklinghausen's disease.