Lymphangioleiomyomatosis
Lymphangioleiomyomatosis
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DOI：
10.1016/j.ccm.2004.05.003
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发表时间：
2004-09-01
影响因子：
5.7
通讯作者：
Glassberg, MK
中科院分区：
文献类型：
--
作者：
Glassberg, MK
摘要淋巴管平滑肌瘤病（LAM）是一种罕见的特发性疾病，主要影响女性。该疾病的特征是支气管周围、血管周围和淋巴周围平滑肌样细胞增生，导致血管和气道阻塞和囊肿形成。肺性LAM的自然史尚不清楚，其临床过程具有显著的多样性。目前在文献中列出了400多篇关于LAM的引用。本文回顾和更新了快速增长的LAM知识。
Lymphangioleiomyomatosis (LAM) is a rare idiopathic disease predominately affecting women. The disease is characterized by peribronchial, perivascular, and perilymphatic proliferation of smooth muscle like cells resulting in vascular and airway obstruction and cyst formation. The natural history of pulmonary LAM is unknown, and it displays remarkable diversity in its clinical course. More than 400 citations are currently listed in the literature for LAM. This article reviews and updates the rapidly expanding knowledge about LAM.