Goldenhar Syndrome With Ankylosis of the Temporomandibular Joint: A Case Report
Goldenhar Syndrome With Ankylosis of the Temporomandibular Joint: A Case Report
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DOI：
10.1213/xaa.0000000000001461
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发表时间：
2021-05-01
期刊：
影响因子：
0.5
通讯作者：
Partyka, Lauren M.
中科院分区：
文献类型：
--
作者：
Partyka, Lauren M.
Goldenhar综合征，或眼耳椎发育不良，约占颅面矮小畸形的10%。这些患者具有与麻醉提供者相关的各种临床特征，包括高弓腭、下颌发育不全、小颌和颞下颌关节（TMJ）畸形。Goldenhar综合征的口腔表现从咬合不正到复杂的颞下颌关节受累不等。在牙科和口腔外科文献之外，很少强调Goldenhar患者TMJ强直的可能性。颞下颌关节强直影响气道管理，麻醉提供者在计划Goldenhar综合征患者的麻醉护理时必须意识到这种临床表型。
Goldenhar syndrome, or oculoauriculovertebral dysplasia, represents approximately 10% of craniofacial microsomia anomalies. These patients have a variety of clinical features that are relevant to anesthesia providers, including a high-arched palate, mandibular hypoplasia, micrognathia, and temporomandibular joint (TMJ) malformation. The oral manifestations of Goldenhar syndrome range from malocclusion to complex TMJ involvement. Outside of the dental and oral surgery literature, the potential for TMJ ankylosis in Goldenhar patients is seldom emphasized. TMJ ankylosis impacts airway management, and anesthesia providers must be aware of this clinical phenotype when planning the anesthetic care of patients with Goldenhar syndrome.