Primary Dedifferentiated Chondrosarcoma of the Lung
Primary Dedifferentiated Chondrosarcoma of the Lung
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DOI：
10.1097/smj.0b013e3181ad6236
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发表时间：
2009-08-01
影响因子：
1.1
通讯作者：
Bou-Khalil, Pierre
中科院分区：
文献类型：
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作者：
Boueiz, Adel;Abougergi, Marwan S.;Bou-Khalil, Pierre
骨骼外去分化软骨肉瘤（DC）是一种罕见的肿瘤，主要发生在头部和颈部。在此，我们描述了一例系统性硬化症患者的肺DC检测，并提出了一个有症状的大量胸腔积液和肺叶实变的胸部成像。据我们所知，这是第一次报告肺软骨肉瘤涉及胸膜和发生与系统性硬化症。此外，这是第二次报告的一个去分化的变种之间的所有报告的情况下，原发性肺软骨肉瘤。
Extraskeletal dedifferentiated chondrosarcomas (DC) are uncommon tumors that predominantly occur in the head and neck. Herein, we describe a case of pulmonary DC detected in a patient with systemic sclerosis and presenting with a symptomatic large pleural effusion and a pulmonary lobar consolidation on chest imaging. To the best of our knowledge, this is the first report of pulmonary chondrosarcoma involving the pleura and occurring in association with systemic sclerosis. Moreover, this is the second report of a dedifferentiated variant among all reported cases of primary lung chondrosarcoma.