Hemophilic pseudotumor. Two cases occurring in siblings.
Hemophilic pseudotumor. Two cases occurring in siblings.
复制标题
血友病假瘤。
DOI：
10.1001/archsurg.1960.01300040053010
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发表时间：
1960
影响因子：
--
通讯作者：
R. Bailey
中科院分区：
文献类型：
--
作者：
J. Abell;R. Bailey
引言 血友病性假瘤是一个描述性术语，包括由于压力下血肿导致骨自发坏死而引起的任何关节外骨质破坏性和增殖性变化。尽管自 1918 年以来仅报告了 17 例此类病例，但我们相信这种情况在血友病患者中可能并不罕见。由于出血性素质及其并发症的发生率不断增加，认识到这一实体很重要。 17 这种病变的不祥 X 线摄影表现提示骨源性肉瘤，多次导致手术干预，随后出现出血、感染和死亡。目的 我们的目的是报告另外两例发生在黑人男性兄弟姐妹中的血友病假瘤病例。通过将这些患者与之前的 17 名患者进行比较，我们希望能够概述骨吸收肿瘤或血友病假瘤的有用描述。我们相信该报告在这两名患者的种族和关系方面是独一无二的；在其他方面它与
Introduction Hemophilic pseudotumor is a descriptive term which includes any extra-articular osseous destructive and proliferative changes due to spontaneous necrosis of bone by hematoma under pressure. Although only 17 such cases have been reported since 1918, we believe the condition probably is not rare among hemophiliacs. Recognition of this entity is important because of increasing incidence of the hemorrhagic diatheses and their complications. 17 The ominous roentgenographic appearance of this lesion, suggestive of osteogenic sarcoma, has repeatedly led to surgical intervention with subsequent hemorrhage, infection, and death. Purpose Our purpose is to report two additional cases of hemophilic pseudotumor occurring in Negro male siblings. By comparing these patients with the previous 17 we hope to outline a useful description of the resorption tumor of bone or pseudotumor of hemophilia. We believe the report is unique as regards race and relationship of these two patients; in other respects it parallels the