Case 47: dural ectasia associated with Marfan syndrome.
Case 47: dural ectasia associated with Marfan syndrome.
复制标题
病例47：与马凡综合征相关的硬脑膜扩张。
DOI：
10.1148/radiol.2233000971
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发表时间：
2002
期刊：
影响因子：
19.7
通讯作者：
Francomano,ClairA
中科院分区：
文献类型：
--
作者：
Ho,NicolaC;Hadley,DonaldW;Jain,PawanK;Francomano,ClairA
病例的体征和症状，沿着影像学检查，提示为马凡氏综合征。这个病例说明了在患有马凡氏综合征的年轻和老年患者中考虑硬膜扩张的重要性，这些患者有腰痛、臀部或腿部神经根性疼痛、腿部无力或尿失禁。硬脊膜扩张可能伴有脊椎前移、脊柱侧凸和椎体侵蚀和/或骨折。这种情况可能与骶前脊膜膨出有关，并可能表现为盆腔肿块。该患者有症状，考虑进行硬脑膜神经外科修复。
DISCUSSIONThe signs and symptoms in this patient, along with the imaging findings, indicated Marfan syndrome. This case illustrates the importance of considering dural ectasia in young and old patients with Marfan syndrome who have low back pain, radicular pain in the buttocks or legs, leg weakness, or urinary incontinence. Dural ectasia may be accompanied by spondylolisthesis, scoliosis, and vertebral erosions and/or fractures. This condition may be associated with an anterior sacral meningocele and may manifest as a pelvic mass. This patient was symptomatic, and neurosurgical repair of the dura was considered.