The Expanding Clinical Spectrum of Torpedo Maculopathy
The Expanding Clinical Spectrum of Torpedo Maculopathy
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DOI：
10.1097/opx.0000000000000181
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发表时间：
2014-04-01
影响因子：
1.4
通讯作者：
Raveendranathan, Praneetha
中科院分区：
文献类型：
--
作者：
Trevino, Richard;Kiani, Salma;Raveendranathan, Praneetha
目的电鳐性黄斑病变是一种先天性、特发性、位于黄斑颞侧的椭圆形脉络膜视网膜色素减退。电鳐病变通常是单侧的，偶尔有视网膜内裂，并可能伴有不同程度的色素沉着。视力通常正常，但病变可能在视野中产生暗点。没有已知的相关全身或眼部异常。诊断是基于识别其特征形状和位置。由于其nonprogressive和一般良性的性质，没有治疗是requires.Case报告两例鱼雷黄斑病变与眼底挖掘。据我们所知，这是首次报道鱼雷样黄斑病变与眼底挖除相关。在1例病例中，视力未受影响，在另1例病例中，视力降至20/50。在这两种情况下，光学相干断层扫描清楚地表明挖掘性质的鱼雷损伤。在病例1中，视力正常，凹陷远离中央凹，但在病例2中，视力为20/50，凹陷侵犯中央凹。在这两种情况下，暗点对应的挖掘regions.Conclusions鱼雷黄斑病变通常是一个良性的条件与正常的视力和视野正常。我们的病例显示鱼雷状黄斑病变可能与眼底的凹陷及视野中的暗点有关。视敏度可能会受到损害，如果挖掘侵犯中央凹。这以前未报道的鱼雷状黄斑病变的临床表现的知识可能有助于提高这种情况的理解和患者的护理障碍。
Purpose Torpedo maculopathy is an idiopathic, congenital, oval-shaped region of chorioretinal hypopigmentation located temporal to the macula. Torpedo lesions are typically unilateral, occasionally harbor an intraretinal cleft, and may be associated with varying degrees of hyperpigmentation. Visual acuity is usually normal, but the lesion may produce a scotoma in the visual field. There are no known associated systemic or ocular abnormalities. Diagnosis is based upon recognition of its characteristic shape and location. Because of its nonprogressive and generally benign nature, no treatment is required.Case Reports Two cases of torpedo maculopathy associated with fundus excavation are presented. To the best of our knowledge, this is the first reported association of torpedo maculopathy with fundus excavation. In one case, the visual acuity remained unaffected and in the other case the visual acuity was reduced to 20/50. In both cases, optical coherence tomography clearly demonstrates the excavated nature of the torpedo lesions. In case 1, where the visual acuity was normal, the excavation is remote from the fovea but in case 2, where the visual acuity was 20/50, the excavation encroaches upon the fovea. In both cases, a scotoma corresponding to the excavated region could be demonstrated.Conclusions Torpedo maculopathy is a usually benign condition associated with normal visual acuity and normal visual fields. Our cases demonstrate that torpedo maculopathy may be associated with excavation of the fundus and a corresponding scotoma in the visual field. Visual acuity may be compromised should the excavation encroach upon the central fovea. Knowledge of this previously unreported clinical manifestation of torpedo maculopathy may aid in advancing the understanding of this condition and the care of patients with the disorder.