Osteogenesis Imperfecta Congenita and Tarda: A Temporal Bone Report
Osteogenesis Imperfecta Congenita and Tarda: A Temporal Bone Report
复制标题
先天性成骨不全和迟发性成骨不全：颞骨报告
DOI：
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发表时间：
1975
期刊：
影响因子：
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通讯作者：
J. Lindsay
中科院分区：
文献类型：
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作者：
J. Zajtchuk;J. Lindsay
The temporal bone report of an operated case of osteogenesis imperfecta tarda is presented. Histological examination confirmed the presence of bilateral fixation of the footplate by otosclerosis as the cause of the conductive hearing loss. Fragility of bony septae in the mastoid and of the stapedial crura were observed. Sensorineural impairment in later years with a reduction in neural elements in the cochlea appear related to the extent and activity of the otosclerotic foci. Additional temporal bone reports of three cases of osteogenesis imperfecta congenita show lack of deposition of the skein-like bone in the endochondral layer, sparse bony septae in marrow spaces and deficiency of the periosteal layer. The stapedial crura were thin and in two cases both were deformed and fractured.
