Nutrition for Children with Epidermolysis Bullosa
Nutrition for Children with Epidermolysis Bullosa
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DOI：
10.1016/j.det.2010.01.010
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发表时间：
2010-04-01
影响因子：
2.4
通讯作者：
Haynes, Lesley
中科院分区：
文献类型：
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作者：
Haynes, Lesley
优化感染抵抗力、生长、性成熟、伤口愈合以及提供最佳的整体生活质量是大疱性表皮松解症儿童的重要管理目标。然而，所有这些目标都依赖于维持最佳营养状态，而在严重类型的疾病中实现这一目标极具挑战性。当营养师或营养师作为多学科团队的重要成员并充分了解患者的情况、家庭动态和预后时，改善营养状况的策略就有最大的成功机会。即使是最协调的饮食干预措施也可能只能产生有限的影响。
Optimization of resistance to infection, growth, sexual maturation, wound healing, and provision of the best possible overall quality of life are important management goals in children with epidermolysis bullosa. However, all these goals rely on the maintenance of optimal nutritional status, and achieving this is extremely challenging in the severe types of the disease. Strategies to improve nutritional status have the best chance of success when the dietitian or nutritionist works as an integral member of the multidisciplinary team and is well informed of patients' situations, family dynamics, and prognoses. Even the best-coordinated dietetic interventions may exert only limited impact.