Rare case of extraskeletal Ewings sarcoma of the sinonasal tract.
Rare case of extraskeletal Ewings sarcoma of the sinonasal tract.
复制标题
鼻窦骨外尤文氏肉瘤的罕见病例。
DOI：
10.4103/0973-1482.95197
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发表时间：
2012
影响因子：
1.3
通讯作者：
J. H. Makannavar
中科院分区：
文献类型：
--
作者：
S. Yeshvanth;K. Ninan;S. Bhandary;Kishan Prasad H Lakshinarayana;Jayaprakash Shetty;J. H. Makannavar
尤文氏肉瘤和原始神经外胚层肿瘤是儿童和青少年常见的小圆细胞肿瘤。这些肿瘤发生在头部和颈部的发病率仅为2- 7%。下颌骨和上颌骨是最常见的部位，而鼻窦道的参与是非常罕见的。我们报告了一例29岁女性鼻窦骨外ES病例，该患者出现鼻塞和鼻衄。患者接受了14个周期的化疗，联合手术和放疗，完全恢复。由于此病例罕见，我们提出分析其临床、组织病理及免疫组化表现，以与其他鼻窦小圆细胞肿瘤鉴别，并作出适当的治疗。
Ewings sarcoma (ES) and primitive neuroectodermal tumor are closely related family of small round cell tumors seen in childhood and adolescence. The incidence of these tumors occurring in the head and neck region is just 2-7%. Mandible and maxilla are the most common sites, whereas involvement of the sinonasal tract is very rare. We report a case of extraskeletal ES of the sinonasal tract in a 29-year-old female who presented with nasal obstruction and epistaxis. The patient was treated with 14 cycles of chemotherapy, combined with surgery and radiotherapy with complete recovery. We present this case due to its rarity, to analyze the clinical, histopathological and immunohistochemical findings, so as to differentiate from other small round cell tumors of the sinonasal tract for appropriate treatment.