Undifferentiated sarcoma of the liver: a single institution experience using a uniform treatment approach.
Undifferentiated sarcoma of the liver: a single institution experience using a uniform treatment approach.
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DOI：
10.1097/mph.0b013e3182331fbe
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发表时间：
2012-04
期刊：
影响因子：
--
通讯作者：
Macy ME
中科院分区：
文献类型：
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作者：
May LT;Wang M;Albano E;Garrington T;Dishop M;Macy ME
未分化(胚胎性)肝肉瘤是一种罕见的恶性肿瘤，最常见于6至10岁的儿童。以前被认为预后不佳，但最近的报告表明，手术切除和辅助化疗相结合的治疗方案可以产生长期的、无病生存。在这篇报告中，我们回顾了五名儿童USL患者，采用统一的切除方法，然后在有适应症的情况下进行辅助化疗和放疗。所有五名患者首次缓解时均无疾病，中位数为53个月。
Undifferentiated (embryonal) sarcoma of the liver (USL) is a rare malignant tumor most commonly seen in children aged 6 to 10 years. Previously believed to carry a poor prognosis, more recent reports indicate that treatment regimens combining surgical resection and adjuvant chemotherapy can yield long-term, disease-free survival. In this report, we review five pediatric patients with USL treated with a uniform approach of resection followed by adjuvant chemotherapy and radiation when indicated. All five patients are disease-free in their first remission at a median of 53 months.