Segmental absence of intestinal musculature (SAIM): a case report in an adult.
Segmental absence of intestinal musculature (SAIM): a case report in an adult.
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DOI：
10.1136/bcr.01.2009.1425
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发表时间：
2009-01-01
期刊：
影响因子：
0.9
通讯作者：
Ibrahim, Hassan
中科院分区：
文献类型：
--
作者：
Aldalati, Omar;Phelan, Cordelia;Ibrahim, Hassan
节段性肠肌肉组织缺失（SAIM）是一种病因不明的罕见疾病。本文介绍了一个成人 SAIM 病例，并回顾了另外三个成人 SAIM 病例。我们的病例涉及一名中年男子，他因胰头疑似肿瘤而接受了惠普尔手术。手术时，偶然发现近端空肠的多余部分并伴有多个大憩室，并将其切除。在组织学检查中，小肠段显示固有肌层局灶性极度变薄，局灶性达到完全缺失。还提交了腹膜活检，显示与陈旧血栓血管一致的变化。
Segmental absence of intestinal musculature (SAIM) is a rare entity of uncertain aetiology. A case of SAIM in an adult is presented, and three other adult cases of SAIM are reviewed. Our case concerns a middle-aged man who underwent a Whipple's procedure for a suspected neoplasm in the head of the pancreas. At surgery, a redundant segment of proximal jejunum with multiple large diverticula was incidentally noted and resected. On histological examination, the small bowel segment showed focal extreme thinning of the muscularis propria, focally amounting to complete absence. A peritoneal biopsy was also submitted which showed changes consistent with an old thrombosed vessel.