The role of Cone beam CT in the evaluation and management of a family with Gardner's syndrome
The role of Cone beam CT in the evaluation and management of a family with Gardner's syndrome
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DOI：
10.1016/j.jcms.2009.06.007
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发表时间：
2009-12-01
影响因子：
3.1
通讯作者：
English, Jeryl D.
中科院分区：
文献类型：
--
作者：
Kamel, Sherif Galal;Kau, Chung How;English, Jeryl D.
加德纳综合征（GS）是一种遗传性常染色体显性遗传性结肠疾病，表现为结肠外表现，如骨瘤、皮肤病变和牙齿异常。骨瘤常见于颅骨、颌骨和鼻旁窦。我们提出了一个家庭的四个姐妹篇与GS的影响范围广泛的异常。锥形束计算机断层扫描（CBCT）在骨瘤和牙齿异常的早期检测和评估中的作用，以及对它们与邻近解剖结构关系的精确评估，在此详细描述。CBCT的仔细解释可能是一个很大的价值，在外科和正畸治疗计划在颌骨病变的存在。由于存在牙瘤和骨密度增加，GS中牙齿问题的管理可能具有挑战性。多学科方法在GS的管理可以达到最佳的治疗效果。(C)2009年欧洲颅颌面外科协会
Gardner's syndrome (GS) is a hereditary autosomal dominant disease of the colon that presents with extra-colonic manifestations such as osteomas, skin lesions and dental abnormalities. Osteomas are commonly found in the skull, jaws and the paranasal sinuses. We present a family of four sisters affected with GS with a wide range of anomalies. The role of Cone beam computed tomography (CBCT) in the early detection and evaluation of osteomas and dental anomalies with precise assessment of their relationship to adjacent anatomic structures is described here in detail. The careful interpretation of CBCT may be of a great value in surgical and orthodontic treatment planning in the presence of jaw lesions. Management of dental problems in GS may be challenging due to the presence of odontomas and increased bone density. A multidisciplinary approach in the management of GS can achieve the best treatment results. (C) 2009 European Association for Cranio-Maxillofacial Surgery