症例 トルコ鞍内から鞍上部に存在した上衣腫の1例
症例 トルコ鞍内から鞍上部に存在した上衣腫の1例
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病例：一例位于蝶鞍内及蝶鞍上方的室管膜瘤。
DOI：
10.11477/mf.1436204374
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发表时间：
2021
期刊：
影响因子：
--
通讯作者：
齋藤 清
中科院分区：
文献类型：
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作者：
橋野 洸平;佐藤 拓;岸田 悠吾;黒見 洋介;喜古 雄一郎;山田 昌幸;丹原 正夫;佐久間 潤;齋藤 清
鞍区和鞍上区的室管膜瘤在现有文献中仅有10例报道。我们描述了一例70岁女性的类似病理，她表现为痴呆症和视觉障碍。磁共振成像显示在鞍区和鞍上区有一混合增强的病灶(最大直径3.5厘米)，并伴有非交通性脑积水。患者在手术前被推定为颅咽管瘤。病变粘连于下丘脑，经鼻内窥镜经蝶窦入路完全切除第三脑室底。组织病理学检查证实为室管膜瘤。虽然她的视力障碍有所改善，但患者术后出现了全垂体功能减退。术后7年未复发。鞍区和鞍上区的室管膜瘤非常罕见，在这类患者中确定术前诊断是具有挑战性的。最大限度的肿瘤切除和长期随访是获得良好预后的关键。
An ependymoma of the sella turcica and the suprasellar region has been described by only 10 reports in the available literature. We describe similar pathology in a 70-year-old woman who presented with dementia and visual disturbance. Magnetic resonance imaging with gadolinium revealed a mixed contrast-enhanced lesion (maximum diameter 3.5 cm) in the sella turcica and suprasellar area associated with a noncommunicating hydrocephalus. The patient was preoperatively presumptively diagnosed with a craniopharyngioma. The lesion was adherent to the hypothalamus, and the third ventricular floor was completely resected via an endoscopic endonasal transsphenoidal approach. Histopathological findings confirmed an ependymoma. Although her visual disturbance improved, the patient developed postoperative panhypopituitarism. She has had no recurrence for 7 years postoperatively. An ependymoma of the sella turcica and the suprasellar region is extremely rare; establishing the preoperative diagnosis is challenging in such patients. Maximum tumor resection and long-term follow-up are essential for good prognosis.