Malignant peripheral nerve sheath tumor: An unusual cause of intussusception
Malignant peripheral nerve sheath tumor: An unusual cause of intussusception
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DOI：
10.1007/s11605-007-0395-5
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发表时间：
2008-09-01
影响因子：
3.2
通讯作者：
Pertsemlidis, David
中科院分区：
文献类型：
--
作者：
Telem, Dana A.;Pertsemlidis, David
恶性周围神经鞘瘤（MPNST）被定义为任何源自周围神经或表现出神经鞘分化的肿瘤。这些肿瘤大多数出现在躯干、四肢或头颈部区域。迄今为止的文献中，发生于胃肠道的 MPNST 病例不到 14 例，仅报道过 2 例发生于小肠的病例，其中 1 例为复发性疾病。在本文中，我们报告了美国首例发生于小肠并表现为肠套叠的 MPNST 病例。
Malignant peripheral nerve sheath tumors (MPNST) are defined as any tumor arising from a peripheral nerve or showing nerve sheath differentiation. The majority of these tumors arise on the trunk, extremities, or head and neck region. The literature to date has fewer than 14 cases of MPNST arising in the gastrointestinal tract, and only two cases were ever reported in the small intestine, one of which was a recurrent disease. In this paper, we report the first US case of an MPNST arising in the small intestine and presenting as intussusception.