Leptomeningeal Interfoliar Enhancement on Vessel Wall MR Imaging as a Unique Radiologic Finding of Susac Syndrome
Leptomeningeal Interfoliar Enhancement on Vessel Wall MR Imaging as a Unique Radiologic Finding of Susac Syndrome
复制标题
血管壁 MR 成像的软脑膜叶间增强是 Susac 综合征的独特放射学发现
DOI：
10.3174/ajnr.a7801
复制
发表时间：
2023
影响因子：
3.5
通讯作者：
H. Chaves
中科院分区：
文献类型：
--
作者：
P. Cardozo;M. Marrodan;A. Gilmore;M. Fiol;H. Chaves
摘要：Susac综合征是一种罕见的影响大脑、视网膜和内耳的疾病，可能由免疫介导的内皮病变引发。诊断基于临床表现和辅助检查结果（脑MR成像，荧光素血管造影和听力测定）。最近，血管壁磁共振成像已显示出增加的敏感性，在检测的细微迹象，实质，软脑膜，前庭耳蜗增强。在这份报告中，我们描述了一个独特的发现，确定使用这种技术在一系列的6例Susac综合征，并讨论其潜在的价值，诊断工作和后续行动。
SUMMARY: Susac syndrome is a rare disorder affecting the brain, retina, and inner ear, probably triggered by an immune-mediated endotheliopathy. Diagnosis is based on clinical presentation and ancillary test findings (brain MR imaging, fluorescein angiography, and audiometry). Recently, vessel wall MR imaging has shown increased sensitivity in the detection of subtle signs of parenchymal, leptomeningeal, and vestibulocochlear enhancement. In this report, we describe a unique finding identified using this technique in a series of 6 patients with Susac syndrome and discuss its potential value for diagnostic work-up and follow-up.