Mucinous adenocarcinoma of the renal pelvis with pseudomyxoma peritonei.
Mucinous adenocarcinoma of the renal pelvis with pseudomyxoma peritonei.
复制标题
DOI：
10.4103/0377-4929.43753
复制
发表时间：
2008-10
影响因子：
1
通讯作者：
V. Shah;G. Amonkar;J. Deshpande;Hemant Bhalekar
中科院分区：
文献类型：
--
作者：
V. Shah;G. Amonkar;J. Deshpande;Hemant Bhalekar
肾盆粘液腺癌是一种极为罕见的肿瘤，文献报道极少。腹膜假性粘液瘤是一种罕见的疾病，其特征是腹膜腔内存在粘性胶状物质。继发于原发粘液性肿瘤，尤其是阑尾和卵巢。我们报告一例35岁女性，自一年半以来一直有右侧隐匿性疼痛的病史。超声(USG)和计算机断层扫描(CT)发现一个大的囊性肿块，大小为15x15x12 cm，延伸至右侧腰椎区域。大体上，整个肾脏被转化为一个15x15x12厘米的囊性肿块，内含重1公斤的胶状粘液物质。组织学上，肿瘤由简单和复杂的腺泡组成，表面上类似于含有丰富细胞外粘蛋白的结肠粘膜。因此，诊断为肾盆粘液性腺癌导致腹膜假性粘液瘤。
Mucinous adenocarcinoma of the renal pelvis is an extremely rare tumor with very few case reports in literature. Pseudomyxoma peritonei is an uncommon condition characterized by the presence of mucinous gelatinous material in the peritoneal cavity. It occurs secondary to primary mucinous neoplasms of particularly the appendix and the ovary. We present a case of a 35-year-old female who had a history of dull aching pain in the right flank since one and a half years. Upon ultrasonography (USG) and computerized tomography (CT) scan, there was a large cystic mass measuring 15x15x12 cm, extending into the right lumbar region. Grossly, the entire kidney was converted into a cystic mass measuring 15x15x12 cm containing gelatinous mucinous material weighing 1 kg. Histologically, the tumor was composed of simple and complex glandular acini together with a superficial resemblance to colonic mucosa with abundant extracellular mucin. Thus, a diagnosis of mucinous adenocarcinoma of the renal pelvis leading to pseudomyxoma peritonei was made.