Embryonal rhabdomyo sarcoma (sarcoma botryoides) of the cervix presenting as a cervical polyp treated with fertility-sparing surgery and adjuvant chemotherapy
Embryonal rhabdomyo sarcoma (sarcoma botryoides) of the cervix presenting as a cervical polyp treated with fertility-sparing surgery and adjuvant chemotherapy
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DOI：
10.1016/j.ygyno.2004.06.049
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发表时间：
2004-10-01
影响因子：
4.7
通讯作者：
Baker, J
中科院分区：
文献类型：
--
作者：
Bernal, KL;Fahmy, L;Baker, J
背景女性生殖道胚胎性横纹肌肉瘤（葡萄状肉瘤）在子宫颈是罕见的。好发于儿童和年轻女性，预后比阴道和子宫葡萄状肉瘤好。我们报告一例胚胎性横纹肌肉瘤（葡萄状肉瘤）表现为子宫颈息肉的19岁女性。肿瘤由不同分化的横纹肌母细胞组成，分散在疏松的粘液样基质中，并在上皮下形成明显的“形成层”。该患者成功地接受了保留生育能力的手术和辅助化疗。认识这个不常见的病变在这个网站和它的临床意义是很重要的，以避免误诊。最近的治疗倾向于保守治疗。(C)2004爱思唯尔公司All rights reserved.
Background. Embryonal rhabdomyosarcoma (sarcoma botryoides) of the female genital tract is rare in the cervix. It tends to occur in children and young women, and appears to have a better prognosis than sarcoma botryoides of the vagina and uterus.Case. We report a case of embryonal rhabdomyosarcoma (sarcoma botryoides) presenting as a cervical polyp in a 19-year-old female. The tumor was composed of rhabdomyoblasts of varying differentiation dispersed within a loose, myxoid stroma, and formed a distinct 'cambium' layer beneath the epithelium. The patient was successfully treated with fertility-sparing surgery and adjuvant chemotherapy.Conclusions. Awareness of this uncommon lesion in this site and its clinical implications is important to avoid misdiagnosis. Therapy has recently inclined towards conservative treatment. (C) 2004 Elsevier Inc. All rights reserved.