PHEOCHROMOCYTOMA ASSOCIATED WITH MULTIPLE NEUROFIBROMATOSIS AND INTRACRANIAL HEMANGIOMA
PHEOCHROMOCYTOMA ASSOCIATED WITH MULTIPLE NEUROFIBROMATOSIS AND INTRACRANIAL HEMANGIOMA
复制标题
DOI：
10.1016/0002-9343(59)90210-4
复制
发表时间：
1959-01-01
影响因子：
5.9
通讯作者：
TALIAFERRO, I
中科院分区：
文献类型：
--
作者：
CHAPMAN, RC;KEMP, VE;TALIAFERRO, I
1.1. Three additional patients with pheochromocytoma associated with multiple neurofibromatosis are reported. A review of the literature since 1952 revealed fourteen additional cases of this association of lesions. This brings the total number of cases known to the authors to thirty-five.2.2. A patient with pheochromocytoma, neurofibromatosis and a cerebellar hemangioma, previously reported from this institution, is described again in the light of present information.3.3. A patient with pheochromocytoma, multiple brain stem hemangiomas, and a family history of both von Hippel-Lindau's disease and multiple neurofibromatosis is reported. The previously reported cases in which pheochromocytoma has been associated with von Hippel-Lindau's disease are reviewed.4.4. The striking similarity of the various neurocutaneous syndromes is re-emphasized and an attempt is made to explain this relationship on an embryological basis. The occurrence of pheochromocytoma in these patients can also be accounted for by this hypothesis.5.5. It is concluded that the association of these familial disorders of the neurectoderm with pheochromocytoma is not only helpful in the clinical diagnosis of pheochromocytoma, but strengthens the concept that they are all related disorders of those structures of ectodermal origin.
