"Absent" pulmonary artery in one adult and five pediatric patients: Imaging, embryology, and therapeutic implications
"Absent" pulmonary artery in one adult and five pediatric patients: Imaging, embryology, and therapeutic implications
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DOI：
10.2214/ajr.179.5.1791253
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发表时间：
2002-11-01
影响因子：
5
通讯作者：
Kelekis, DA
中科院分区：
文献类型：
--
作者：
Apostolopoulou, SC;Kelekis, NL;Kelekis, DA
OBJECTIVE.本文的目的是提出一系列的临床和影像学表现的“缺席”肺动脉。来自6例患者的数据（5例单侧病例和1例双侧病例）提供了关于其胚胎学的证据，并说明了手术干预的治疗意义。在我们的系列中，我们发现肺动脉缺如的解剖结构与远端导管起源和近端第六主动脉弓的复旧一致。肺动脉缺如是一个独特的胚胎学实体，需要早期发现和详细调查。在选定的患者中，早期手术干预可能是合理的。
OBJECTIVE. The purpose of this article is to present serial clinical and imaging findings for the "absent" pulmonary artery. Data from six patients with this condition (five unilateral cases and one bilateral case) provide evidence concerning its embryology and illustrate the therapeutic implications of surgical intervention.CONCLUSION. In our series, we found the anatomy of the absent pulmonary artery to be consistent with a distal ductal origin and involution of the proximal sixth aortic arch. The absent pulmonary artery is a distinct embryologic entity that requires early detection and detailed investigation. Early surgical intervention may be justified in selected patients.