Polyostotic fibrous dysplasia with gigantism and huge pelvic tumor: a rare case of McCune-Albright syndrome.
Polyostotic fibrous dysplasia with gigantism and huge pelvic tumor: a rare case of McCune-Albright syndrome.
复制标题
多骨性纤维发育不良伴巨人症和巨大盆腔肿瘤：麦库恩-奥尔布赖特综合征的罕见病例。
DOI：
10.1007/s10147-010-0127-9
复制
发表时间：
2011
期刊：
影响因子：
--
通讯作者：
Nakamura A.
中科院分区：
文献类型：
--
作者：
Sakayama K;Sugawara Y;Kidani T;Fujibuchi T;Kito K;Tanji N;Nakamura A.
我们报告一例罕见的多骨纤维发育不良伴内分泌功能亢进，人生长激素升高，血清催乳素正常。在性别、体型、内分泌功能、GNAS基因等方面与麦库内-奥尔布赖特综合征存在一定的差异。盆腔肿瘤呈快速生长，影像学上怀疑为恶性转化；然而，本病例未发生恶性变化。
We report a rare case of polyostotic fibrous dysplasia on endocrine hyperfunction with elevated human growth hormone and normal serum level of prolactin. There were some differential points of gender, gigantism, endocrine function, and GNAS gene from McCune–Albright syndrome. Malignant transformation was suspected in the pelvic tumor from imaging because rapid growth of the tumor by imaging was observed; however, no malignant change occurred in this case.