The pattern of shortening of the bones of the hand in PHP and PPHP--A comparison with brachydactyly E, Turner Syndrome, and acrodysostosis.
The pattern of shortening of the bones of the hand in PHP and PPHP--A comparison with brachydactyly E, Turner Syndrome, and acrodysostosis.
复制标题
PHP 和 PPHP 中手骨缩短的模式——与 E 型短指畸形、特纳综合征和肢端骨质疏松症的比较。
作者：
A. Poznanski;E. Werder;A. Giedion;Allan J. Martin;Helen Shaw
评估了假性甲状旁腺功能减退症（PHP）、假性甲状旁腺功能减退症（PPHP）和肢端骨质疏松症病例中手骨长度变化的模式。测量每块手骨的长度，并与年龄和性别的适当平均值进行比较。由此生成的模式轮廓显示，PHP 和 PPHP 的模式轮廓几乎相同，并且与肢端成骨不全中看到的模式轮廓相似，除了在后一种情况下看到的骨头尺寸小得多。 PHP和PPHP很可能是同一实体的不同表现，肢端骨性早闭也可能与它们有关。 E 型短指畸形在放射学上与 PHP-PPHP 综合征无法区分。
The patterns of length alterations in the hand bones in cases of pseudohypoparathyroidism (PHP), pseudopseudohypoparathyroidism (PPHP), and acrodysostosis were evaluated. The length of each of the hand bones was measured and compared to appropriate means for age and sex. The pattern profiles thus generated showed that those for PHP and PPHP are almost identical, and are similar to that seen in acrodysostosis, except for the much smaller size of the bones seen in the latter condition. PHP and PPHP are probably differend manifestations of the same entity, and acrodysostosis may also be related to them. Brachydactyly E is indistinguishable radiologically from the PHP-PPHP syndrome.