A Case of Alport Syndrome Associated with Recurrent Stanford Type B Aortic Dissections.
A Case of Alport Syndrome Associated with Recurrent Stanford Type B Aortic Dissections.
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与复发性斯坦福大学主动脉解剖相关的ALPORT综合征病例。
DOI：
10.3400/avd.cr.22-00010
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发表时间：
2022-06-25
影响因子：
0.8
通讯作者：
中科院分区：
文献类型：
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作者：
Alport综合征通常以由于IV型胶原蛋白产生异常而导致的肾功能障碍和听力损失为特征。在这项研究中，我们报告了一个罕见的情况下，复发性主动脉夹层，发展在一个年轻的病人与Alport综合征在很短的时间。我们通过文献综述讨论了Alport综合征和主动脉夹层之间的关系，并强调需要定期随访Alport综合征患者，以早期发现主动脉疾病。
Alport syndrome is often characterized by renal dysfunction and hearing loss due to abnormalities in type IV collagen production. In this study, we report a rare case of recurrent aortic dissections that developed in a young patient with Alport syndrome over a short period. We discuss the associations between Alport syndrome and aortic dissection with a literature review and emphasize the need for regular follow-up of patients with Alport syndrome for early detection of aortic disease.