Severe cardiac arrhythmias in young patients with myotonic dystrophy type 1
Severe cardiac arrhythmias in young patients with myotonic dystrophy type 1
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DOI：
10.1212/01.wnl.0000144343.91136.cf
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发表时间：
2004-11-23
期刊：
影响因子：
9.9
通讯作者：
Duboc, D
中科院分区：
文献类型：
--
作者：
Bassez, G;Lazarus, A;Duboc, D
心脏快速性心律失常很少被研究的年轻患者强直性肌营养不良1型（DM1）。作者在11例年龄在10至18岁的患者中观察到严重的心律紊乱。心动过速事件比冲动传导障碍更常见。在人群中观察到CTG扩增的广泛变化。由于体育锻炼是一个突出的致糖尿病因素，系统的运动试验与心电图监测可能是指在年轻的DM 1患者。
Cardiac tachyarrhythmias have rarely been studied in young patients with myotonic dystrophy type 1 (DM1). The authors observed major cardiac rhythm disturbances in 11 patients aged 10 to 18 years. Tachyarrhythmic events were more frequent than impulse conduction disorders. Wide variations in CTG expansion were observed among the population. Since physical exercise was a prominent arrhythmogenic factor, systematic exercise tests with EKG monitoring may be indicated in young patients with DM1.