Multiple inflammatory fibrosarcoma of the abdominal cavity in a child.
Multiple inflammatory fibrosarcoma of the abdominal cavity in a child.
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儿童腹腔多发性炎性纤维肉瘤。
DOI：
10.1002/(sici)1096-911x(199609)27:3
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发表时间：
1996
期刊：
影响因子：
--
通讯作者：
A. Garaventa
中科院分区：
文献类型：
--
作者：
M. Conte;C. Milanaccio;M. Nantron;E. Castagnola;G. Fratino;G. Cuneo;M. Brisigotti;A. Garaventa
炎症性纤维肉瘤是儿童时期的一种罕见疾病。在腹部位置，其行为通常具有侵袭性并可能发生转移。我们报告一例患有腹部炎性纤维肉瘤的 3 岁女性，根治性手术 1 个月后复发。化疗无效，我们仅使用 α-IFN 就使疾病得到了短暂的稳定。我们的病例证实了这种肿瘤的潜在恶性肿瘤及其对治疗的抵抗力。值得注意的是，α-IFN 治疗改善了该儿童 4 个月的生活质量。
Inflammatory fibrosarcoma is a rare condition in childhood. In the abdominal location, its behaviour is often aggressive and potentially metastasizing. We report a case of a 3-year-old female with abdominal inflammatory fibrosarcoma who relapsed after 1 month from radical surgery. Chemotherapy was ineffective, and we registered a brief stabilisation of disease only with alpha-IFN. Our case confirms the potential malignancy of this tumour and its resistance to treatment. It is noteworthy that the therapy with alpha-IFN improved the quality of life in this child for 4 months.