Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity.
Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity.
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DOI：
10.4103/0976-9668.127347
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发表时间：
2014-01
期刊：
影响因子：
--
通讯作者：
Verma R
中科院分区：
文献类型：
--
作者：
Arul AS;Verma S;Arul AS;Verma R
横纹肌肉瘤是一种恶性肿瘤，由肿瘤性间充质细胞组成，具有不同程度的横纹肌细胞分化。大多数病例发生在10岁以下的儿童中，在成人中非常罕见。此外，在成人中，典型的小儿横纹肌肉瘤变体（胚胎和腺泡亚型）发生频率较低，并表现出对内脏的偏好，其次是头部和颈部区域。本文报告一例罕见的胚胎性横纹肌肉瘤，发生于一位36岁男性颊黏膜。正确的诊断和组织学亚型的识别是至关重要的，在这种疾病的治疗，因为治疗是不统一的，因为这种肿瘤在成人人群中的罕见性在文献中。
Rhabdomyosarcoma is a malignant tumor composed of neoplastic mesenchymal cells, with varying degrees of striated muscle cell differentiation. With most cases occurring in children younger than 10 years, it is remarkably rare in adults. Further in adults, the typical pediatric rhabdomyosarcoma variants (embryonal and alveolar sub-types) occur less frequently and exhibit predilection for viscera followed by the head and neck region. A rare case of embryonal rhabdomyosarcoma arising from the buccal mucosa in a 36-year old male patient is herewith reported. Recognition of the correct diagnosis and histological sub-type is of critical importance in the therapy of this disease, since the treatment is not uniform in the literature because of the rarity of this neoplasm in the adult population.