Pulmonary artery sarcomas. A review and report of a case.
Pulmonary artery sarcomas. A review and report of a case.
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肺动脉肉瘤。
DOI：
--
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发表时间：
1985
影响因子：
4.6
通讯作者：
Good Ra
中科院分区：
文献类型：
--
作者：
Baker Pb;Good Ra
我们检查了一例原发性肺动脉肉瘤，复习了以前在英文文献中报道的45例，并特别注意了其病理特征。这些肉瘤累及肺动脉干、左右主肺动脉、肺动脉瓣和右室流出道。它们沿动脉内膜有明显的血管内生长。肺部受累通常是通过肺血管直接延伸或远处转移。这些肉瘤含有各种异源成分，骨、软骨和纤维组织的区域可以分化得非常好。了解这些肉瘤的生物学行为和病理特征将有助于这些肉瘤的治疗。
: We examined a case of primary pulmonary artery sarcoma and reviewed 45 cases that we found previously reported in the English literature, with particular attention given to the pathologic features. These sarcomas involve the pulmonary arterial trunk, left and right main pulmonary arteries, pulmonary valve, and right ventricular outflow tract. They have prominent intravascular growth along the arterial intima. Lung involvement commonly occurs by direct extension through the pulmonary vasculature or by distant metastases. These sarcomas contain a variety of heterologous components and areas of bone, cartilage, and fibrous tissue may be remarkably well-differentiated. Management of these sarcomas will be aided by an understanding of their biologic behavior and pathologic features.