[Unilateral left superior vena cava in absent right superior vena cava. Modern imaging diagnosis and clinical relevance].

[Unilateral left superior vena cava in absent right superior vena cava. Modern imaging diagnosis and clinical relevance].
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[单侧左上腔静脉缺如右上腔静脉。

DOI:
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发表时间:
1994
期刊:
Zeitschrift für Kardiologie
影响因子:
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通讯作者:
H. Kallfelz
H. Kallfelz
中科院分区:
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文献类型:
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作者:
H. Kaemmerer;M. Prokop;E. Schirg;M. Emter;C. Hesel;W. Daniel;H. Kallfelz

文献摘要

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本文描述了一位64岁的左上腔静脉持续性和右侧上腔静脉缺失的患者的心脏学和影像学表现。持续性左上腔静脉(PLSVC)的存在被认为是最常见的系统性静脉回流异常之一。它最常与右侧上腔静脉合并,只有在极少数情况下,右侧上腔静脉缺失或闭锁。这种畸形通常与其他先天性心脏缺陷有关,但没有主要的血流动力学意义。这种变异可能导致静脉置管、起搏器电极插入或体外循环时的困难。诊断可通过血管造影、计算机断层扫描和核磁共振成像证实。
Cardiological and radiological findings in a 64-year-old patient with persistent left superior vena cava and absent right-sided superior vena cava are described. Presence of a persistent left superior vena cava (PLSVC) is considered to be one of the most frequent anomalies of the systemic venous return. It occurs most often in association with a right-sided superior vena cava and only in rare cases with an absent or atretic right-sided superior vena cava. This malformation is often associated with other congenital heart defects, but without major hemodynamic significance. The variation may cause difficulties in venous catheterization, pacemaker electrode insertion or during cardiopulmonary bypass. The diagnosis can be confirmed by angiography, computed tomography and nuclear magnetic resonance imaging.