Sporadic Creutzfeldt-Jakob disease presenting with nonconvulsive status epilepticus
Sporadic Creutzfeldt-Jakob disease presenting with nonconvulsive status epilepticus
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DOI：
10.1016/j.yebeh.2004.06.019
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发表时间：
2004-10-01
影响因子：
2.6
通讯作者：
Beydoun, A
中科院分区：
文献类型：
--
作者：
Cohen, D;Kutluay, E;Beydoun, A
克雅氏病 (CJD) 是一种罕见的朊病毒病，其特征是人类海绵状脑病。尽管肌阵挛、痴呆和周期性脑电图活动的特征三联征很容易识别，但该疾病的异常表现可能具有挑战性，并造成诊断困境。我们报道了一名 26 岁患者发生的克雅氏病病例，该患者出现继发于非惊厥性癫痫持续状态的接受性（韦尼克氏）失语症。 (C) 2004 Elsevier Inc. 保留所有权利。
Creutzfeldt-Jakob disease (CJD) is a rare prion disease characterized by a spongiform encephalopathy in humans. Although the characteristic triad of myoclonus, dementia, and periodic EEG activity is easy to recognize, unusual manifestations of the disease may be challenging and create a diagnostic dilemma. We report a case of CJD that occurred in a 26-year-old patient who presented with a receptive (Wernicke's) aphasia secondary to nonconvulsive status epilepticus. (C) 2004 Elsevier Inc. All rights reserved.