Recurrent primary cardiac osteosarcoma: a case report and literature review
Recurrent primary cardiac osteosarcoma: a case report and literature review
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DOI：
10.1007/s11748-013-0236-2
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发表时间：
2014-03-01
影响因子：
1.2
通讯作者：
Stella, Franco
中科院分区：
文献类型：
--
作者：
Dell'Amore, Andrea;Asadi, Nizar;Stella, Franco
原发性心脏恶性肿瘤非常罕见。在恶性肿瘤中，肉瘤占首位。特别是原发性心脏骨肉瘤是非常罕见的。据我们所知，全世界只有42例报告。心脏恶性肿瘤通常需要复杂的手术，因为难以完全切除肿瘤与可接受的游离手术切缘，因为接近重要结构。目前心脏肉瘤的综合治疗策略仍不理想，特别是手术治疗效果往往不令人满意。我们报告一例复发性原发性心脏骨肉瘤的年轻男性谁接受了经胸骨右肺切除术和广泛切除的左，右心房，然后重建与异源心包在体外循环下。患者于术后6个月因局部和全身疾病复发死亡。
Primary malignant cardiac tumors are very rare. Among malignant tumors, sarcomas occupy first place. In particular, primary cardiac osteosarcoma is extremely rare. To the best of our knowledge, only 42 cases have been reported worldwide. Cardiac malignant tumors usually require complex operations due to the difficulty in completely removing the tumor with acceptable free surgical margins and because of the proximity to vital structures. The current multimodality treatment strategies for cardiac sarcoma are still suboptimal, and surgery in particular frequently has unsatisfactory results. We report a case of recurrent primary cardiac osteosarcoma in a young male who underwent trans-sternal right pneumonectomy and a wide resection of the left and right atrium followed by reconstruction with heterologous pericardium under extracorporeal circulation. The patient died 6 months after the operation due to local and systemic disease recurrence.