First case of pneumatosis cystoides intestinalis in adult dermatomyositis.

First case of pneumatosis cystoides intestinalis in adult dermatomyositis.
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第一例成人皮肌炎肠囊肿积气症。

DOI:
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发表时间:
1993
影响因子:
3.9
通讯作者:
N. Peigney
N. Peigney
中科院分区:
医学2区
文献类型:
--
作者:
E. Pasquier;M. Wattiaux;N. Peigney

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我们描述了第一例成人皮肌炎(DM)中肠囊肿积气的病例。当发生肠囊肿积气时,该患者的糖尿病已缓解多年。它的发现与间质性肺病的发现同时发生。肠囊肿积气的总体病程是良性的。我们讨论了肠道和肺部受累的机制,并假设血管炎可能是潜在的过程。
We describe the first case of pneumatosis cystoides intestinalis in dermatomyositis (DM) of an adult. Our patient had been in remission of her DM for years when pneumatosis cystoides intestinalis occurred. Discovery of it was concomitant with that of interstitial lung disease. The overall course of pneumatosis cystoides intestinalis was benign. We discuss the mechanism of bowel and lung involvement and hypothesize that vasculitis could be the underlying process.