Polyunsaturated fatty acids reverse the lysosomal storage and accumulation of subunit 9 of mitochondrial F1F0-ATP synthase in cultured lymphoblasts from patients with Batten disease.
Polyunsaturated fatty acids reverse the lysosomal storage and accumulation of subunit 9 of mitochondrial F1F0-ATP synthase in cultured lymphoblasts from patients with Batten disease.
复制标题
多不饱和脂肪酸可逆转 Batten 病患者培养的淋巴母细胞中线粒体 F1F0-ATP 合酶 9 亚基的溶酶体储存和积累。
DOI:
10.1023/a:1005387608456
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发表时间:
1997
影响因子:
4.2
通讯作者:
Boustany,RM
中科院分区:
文献类型:
--
作者:
Bennett,MJ;Boriack,RL;Boustany,RM
MATERIALS AND METHODSThe method for lymphoblast tissue culture was as previously described (Boriack et al 1995). The cell lines utilized for these studies were from patients homozygous for the common 1kb genomic deletion (Lerner et al 1995). The cells were grown in Opti-Mem