Aorto-left ventricular tunnel with anomalous origin of right coronary artery and bicuspid aortic valve: a case report.
Aorto-left ventricular tunnel with anomalous origin of right coronary artery and bicuspid aortic valve: a case report.
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右冠状动脉和二叶式主动脉瓣起源异常的主动脉-左心室通道：一例报告
DOI：
10.1186/s13019-018-0770-1
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发表时间：
2018-06-28
影响因子：
1.6
通讯作者：
Zou C
中科院分区：
文献类型：
--
作者：
Ma X;Li J;Zhang Q;Kong X;Yuan G;Wang Z;Zou C
研究背景主动脉-左心室隧道（ALVT）是一种罕见的先天性心外通道，连接升主动脉和左心室。我们报告一位5岁女性患者，被诊断为右冠状动脉起源异常（AORCA）和主动脉瓣二叶化（BAV）的ALVT，之前被误诊为BAV触发的主动脉瓣返流（AR）。此外，一个特殊的模式ALVT证实在这种情况下，在手术过程中，隧道形成的两个主动脉瓣叶的根部之间的分离在舒张period.ConclusionsALVT与AORCA和BAV是临床上罕见的和ALVT的异常隧道可以形成的两个主动脉瓣叶的根部之间的差距。此外，ALVT合并BAV可能容易导致BAV引起的主动脉瓣返流的不准确诊断。应提醒心脏外科医生鉴别诊断ALVT伴BAV和孤立性二叶式主动脉瓣（BAV）导致主动脉瓣返流（AR）。
BackgroundAorto-left ventricular tunnel (ALVT) is a rare congenital extracardiac channel that connects the ascending aorta to the left ventricle. To our knowledge, no case has been thus far reported as ALVT with both anomalous origin of right coronary artery (AORCA) and bicuspid aortic valve (BAV).Case presentationWe reported a case of a 5-year-old female diagnosed as ALVT with accompanying AORCA and BAV which had been previously misdiagnosed as aortic regurgitation (AR) triggered by BAV. Additionally, a special modality of ALVT was confirmed in this case during the surgery in which the tunnel was formed by the separation between the roots of two aortic leaflets during the diastolic period.ConclusionsALVT with both AORCA and BAV is clinically uncommon and the aberrant tunnel in ALVT can be formed by the gap between the roots of two aortic leaflets. Besides, ALVT with BAV might easily lead to an inaccurate diagnose as aortic regurgitation caused by BAV. Cardiac surgeons should be alerted for differential diagnosis of ALVT with BAV and isolated bicuspid aortic valve (BAV) causing aortic regurgitation (AR).
影响因子：
0.7
作者：
Kathare P;Subramanyam RG;Dash TK;Muthuswamy KS;Raghu K;Koneti NR
通讯作者：
Koneti NR
影响因子：
24
作者：
Martins, JD;Sherwood, MC;Keane, JF
通讯作者：
Keane, JF