Group III Möbius syndrome: CT and MR findings.
Group III Möbius syndrome: CT and MR findings.
复制标题
III 类莫比乌斯综合征：CT 和 MR 结果。
DOI：
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发表时间：
1990
期刊：
影响因子：
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通讯作者：
P. C. Shekar
中科院分区：
文献类型：
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作者：
M. Kuhn;H. Clark;A. Morales;P. C. Shekar
莫比乌斯综合征是一种先天性神经肌肉疾病，其特征是无法外展眼睛和面部无力[1]。根据原发性异常是否为弥漫性（第1组）、外展神经和面神经（第II组）或核（第III组）或位于CNS外（第IV组），将其分为四组[2]。尽管已报告了与莫比乌斯综合征相关的肌肉骨骼异常的放射学结果[3]，但尚未发表原发性CNS异常的既往影像学研究。我们报告一例儿童的临床和病理证据第III组莫比乌斯综合征的CT和MR研究表明，发育不良的脑干和钙化的外展神经核：ei。提出了放射学-病理学相关性。
Mobius syndrome is a congenital neuromuscular disorder characterized by both inability to abduct the eyes and facial weakness [1] . It is classified into four groups on the basis of whether the primary abnormalities are diffuse (group 1), in the abducens and facial nerves (group II), or nuclei (group Ill), or lie outside the CNS (group IV) [2]. Although the radiologic findings of the musculoskeletal abnormalities associated with Mobius syndrome have been reported [3] , no prior imaging studies of the primary CNS abnormalities have been published. We report a case of a child with clinical and pathologic evidence of group Ill Mobius syndrome whose CT and MR studies showed a hypoplastic brainstem and calcification in the abducens nerve nuc:ei . Radiologic-pathologic correlation is presented .